Case Report
Year: 2019 | Month: October | Volume: 9 | Issue: 10 | Pages: 271-274
Sclerosing Epithelioid Fibrosarcoma of Thigh: Need for Timely Diagnosis and Aggressive Management
Suhaib Rawoot
Chief Resident, Department of General Surgery, Grant Medical College & Sir JJ Group of Hospitals, Mumbai-400008.
ABSTRACT
Sclerosing epithelioid fibrosarcoma (SEF) is a rare soft tissue sarcoma occurring in the extra osseous sites. They account to less than 1 % of all soft tissue sarcomas. Only 89 cases of SEF have been reported till date. We hereby present a rare case of SEF in a 17 year old male who presented with a swelling in the right thigh of 2 months duration. Fine needle aspiration cytology of the swelling revealed it to be a spindle cell tumour. He underwent wide local excision. Histopathology and immuno histochemistry proved it to be sclerosing epithelioid fibrosarcoma. A case report and review of literature is presented below. This is also the first case to be reported from the Indian subcontinent to the best of our knowledge.
Key words: Sclerosing epithelioid fibrosarcoma, timely diagnosis, aggressive management