Case Report
Year: 2021 | Month: June | Volume: 11 | Issue: 6 | Pages: 226-230
DOI: https://doi.org/10.52403/ijhsr.20210635
Lymphangioleiomyomatosis Unusual Cause of Spontaneous Pneumothorax
Lamya Al Aamri1, Raafat Dahrouj1, Nasser Al Awaid2, Rubyath Rajib3
1Internal Medicine Specialist, Sultan Qaboos Hospital, Salalah, Oman.
2Consultant Pulmonologist, Head of Department of Medicine, Sultan Qaboos Hospital, Salalah.
3Senior Consultant, Histopathologist, Sultan Qaboos Hospital, Salalah.
Corresponding Author: Lamya Al Aamri
ABSTRACT
Lymphangioleiomyomatosis (LAM) is a rare multisystem disease, predominately affect premenopausal female. LAM could be an inherited disease associated with Tuberous Sclerosis Complex syndrome or sporadic. Most common pulmonary symptoms are dyspnea and pneumothorax. We report 31- year female, presented with right-side pneumothorax chest drainage was inserted. Further investigation revealed multiple cystic lesions in chest computed tomography images suggestive of LAM disease. She underwent video-assisted thoracoscopic surgery (VATs) to obtain a lung biopsy. Histopathology lung tissue confirms pulmonary Lymphangioleiomyomatosis.
Key words: Lymphangioleiomyomatosis; Tuberous Sclerosis Complex syndrome; video-assisted thoracoscopic surgery.